Radiological manifestation of familial acute necrotizing encephalopathy with RANBP2 mutation in a Far-East Asian family
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چکیده
منابع مشابه
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Symmetric change of the entire area of the bilateral thalami, as with panthalamic lesions, plus involvement of other regions in the brain rarely occurs to previously healthy children. The term, acute necrotizing encephalopathy of childhood, has recently been proposed. Its clinical, radiological, and pathological features are described. This disease predominantly affects infants and young childr...
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acute necrotizing encephalopathy of childhood (anec) is a specific type of encephalopathy. after viral infection, it can be diagnosed by bilateral symmetrical lesions that are predominantly observed in thalami & brainstem of infants & children. although, it is commonly occurred in japanese and taiwanese population. the goal of this article is to report a rare case of anec in north part of ira...
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ژورنال
عنوان ژورنال: Medicine
سال: 2021
ISSN: 0025-7974,1536-5964
DOI: 10.1097/md.0000000000025171